Criss-cross heart which is a cardiac malformation caused by abnormal rotation of the ventricles early in embryonic development, is rare but a double outlet of right ventricle in priss-cross heart is very rare. We experienced a case of criss-cross heart which is situs solidus, concordant atrioventricular connection and double outlet of rig t ventricle with remote ventricular septal defect of perimembranous inlet type. A 4-years old female was diagnosed as a double outlet of right ventricle in criss-cross heart after echocardiography, cardiac catheterization and cardiac angiography. The surgical correction was a intraventricular reconstruction of left ventricular outflow with 314 circle of 20 mm Hemashield vascular graft from the ventricular septal defect to the aorta. The patient had a temporary atrioventricular block but was recovered uneventfully, and a postoperative echocardiogram showed no left ventricular outflow obstruction, no intracardiac shunt.
Criss-Cross heart by abnormal rotation of bulboventricular loop:diaqnostic considerations for complex cardiac anomaly ,
Ando M;Takao A;Cho E;Vehara K;Nihmuia I ,
Proceedings of the pediatric Circulation Society / v.,pp., 1974
The pathologic anatomoy of mixed levocardia: A review of thirteen cases of atrial or ventricular inversion with or without corrected-transposition ,
Lev M;Rowlatt U.F ,
Am J Cardiol. / v.9,pp.216-263, 1961