초록

7년전 누두흉으로 Ravitch수술을 받은 13세 남아가 이차성 전흉벽기형과 운동시 호흡곤란(NYHA II)을 주소로 내원하였다. 술전 심초음파상 이차성 심방중격결손이 진단되었고, 폐기능검사상 WC가 2.03 L(72%), FEVI이 1.82 L(71%)로 감소된 것외에는 술전 검사상 이상소견은 없었다. 수술은 앙와위에서 흉골을 보존한 채 정 중흉절개를 통해 흉근판을 만든후 기형늑연골 잔유물과 섬유조직을 제거하여 이차성 전흉벽기형을 교정한 후 흉골을 90$^{\circ}$로 세움으로써 개심술을 위한 시야를 확보하여 심방중격결손을 동시에 교정하였다. 술후 1일째 급성호흡부전이 있어 기관내 재삽관 및 기계호흡을 시행하였고 술후 6일째 인공호흡기를 제거하였다. 환아는 합병증없이 회복되어 술후 19일째 퇴원하였다.

Abstract

A 13-year-old boy presented with anterior chest wall depression and dyspnea on exertion(NYHA II). He underwent Ravitch operation for pectus excavatum 7 years ago. A preoperative echocardiographic study revealed secundum atrial septal defect. He had no other abnormality of laboratory test, except FVC and FEVI were decreased into 2.03 L(7 %) and 1.82 L(71 %). He underwent repair of secondary anterior chest wall deformity and secundum atrial septal defect. We used unique method, raising sternum at right angle to secure good operative field for open heart surgery. Acute respiratory insufficiency was developed on postoperative day 1. Mechanical ventilation was applied which could be weaned on postoperative day 6 and thereafter hospital course was uneventful without any other sequale. He was discharged on postoperative day 19.

주제어

#관흉벽기형(누두흉)   #선천성심장질환(심장중격결손)  

참고문헌 (7)

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이 논문을 인용한 문헌 (1)

1. 2001. "Simultaneous Repair of Pectus Excavatum and Secundum Atrial Septal Defect" 大韓胸部外科學會誌 = The Korean journal of thoracic and cardiovascular surgery, 34(10): 784~786  원문보기 상세보기