사엽성 대동맥판막은 매우 드문 선천적 기형의 하나로써 심한 대동맥판막페쇄부전의 한 원인으로 알려져 있다. 저자들은 사엽성 대동맥판막과 동반된 심한 대동맥판막폐쇄부전으로 수술을 받은 5명의 환자를 보고한다. 모든 환자들에서 수술 중에 진단이 가능하였다. 환자들 중 2명에서는 감염성 심내막염이 동반되었다. Hurwitz and Roberts 분류법상 2명은 d형, 2명은 a형, 그리고 1명은 c형이었다.
Quadricuspid aortic valve is a rare congenital abnormality but it is well recognized as the cause of significant aortic regurgitation. We describe 5 patients who underwent surgery for severe aortic regurgitation associated with quadricuspid valve. In all patients, this abnormality had been incidentally detected during surgery. Two of the patients had infective endocarditis. In accordance with the Hurwitz and Roberts classification, two valves were type d, two were type a, and one was type c.
Davia JE, Fenoglio JJ, DeCastro CM, McAllister HA Jr, Cheitlin MD. Quadricuspid semilunar valves. Chest 1977; 72:186-9
Fernandez B, Duran AC, Martire A, Lopez D, Sans-Coma V. New embryological evidence for the formation of quadricuspid aortic valves in the Syrian hamster (Mesocricetus auratus). J Comp Pathol 1999;121:89-94
Feldman BJ, Khanderia BK, Warnes CA, Seward JB, Taylor CL, Tajik AJ. Incidence, description and functional assessment of isolated quadricuspid aortic valves. Am J Cardiol 1990;65:937-8
Simonds JP. Congenital malformations of the aortic and pulmonary valves. Am J Med Sci 1923;166:584-95
Hurwitz LE, Roberts WC. Quadricuspid semilunar valve. Am J Cardiol 1973;31:623-6
Janssens U, Klues HG, Hanrath P. Congenital quadricuspid aortic valve anomaly associated with hypertrophic nonobstructive cardiomyopathy: a case report and review of the literature. Heart 1998;78:83-7