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Biomedicine & pharmacotherapy = Biomédecine & pharmacothérapie, v.45 no.9, 1991년, pp.379 - 382
Jacob, F. (Hematology-Oncology Department and Research on Cancer and Blood Disorders, Centre Hospitalier de Luxembourg, L-1210, Luxembourg, Germany) , Ries, F. , Dicato, M.
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Human spongiform encephalopathies (HSE) are uncommon neurodegenerative diseases of unknown etiology. Whilst numerous observations provide arguments for an infectious disorder mediated by an unconventional agent of the so-called prion-type, the recent discovery of predisposing allelic variants sugges...
Resume - Les maladies a prion chez l'homme. Les encephalopathies spongiformes humaines sont des maladies neuro-degeneratives rares dont la pathogenie reste inconnue. Alors que de nombreuses observations plaident en faveur d'une etiologie infectieuse mediee par un agent contaminant de type prion. la decouverte recente de variants alleliques predis-posants permet d'envisager un mecanisme genetique a l'origine de ces affections.
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