Mirás Veiga, Alicia
(Department of Pediatric Intensive Care Unit, Hospital Universitario de Burgos, Burgos, Spain)
,
Moreno, David Conejo
(Department of Pediatric Neurology, Hospital Universitario de Burgos, Burgos, Spain)
,
Menéndez, Ana Isabel Gómez
(Department of Neurophysiology, Hospital Universitario de Burgos, Burgos, Spain)
,
Siscart, Ignacio Muñoz
(Department of Psychiatry, Hospital Universitario de Burgos, Burgos, Spain)
,
Fernández, Marta Del Olmo
(Department of Pediatrics, Hospital Rí)
,
Sánchez, Esteban Gómez
(o Carrió)
,
González, María García
(n, Palencia, Spain)
,
Sáez, Fernando Gómez
(Department of Pediatric Intensive Care Unit, Hospital Universitario de Burgos, Burgos, Spain)
Febrile infection–related epilepsy syndrome (FIRES) is a rare condition which evolves into refractory status epilepticus (SE), with poor outcome in most cases. Conventional antiepileptic drugs fail to control SE in FIRES patients. We report the case of a previously healthy 4-year-old boy who w...
Febrile infection–related epilepsy syndrome (FIRES) is a rare condition which evolves into refractory status epilepticus (SE), with poor outcome in most cases. Conventional antiepileptic drugs fail to control SE in FIRES patients. We report the case of a previously healthy 4-year-old boy who was diagnosed with FIRES. One week after pharyngitis and high fever he started seizures, followed by refractory SE. Benzodiazepines, phenytoin, high-dose barbiturates that induce burst suppression, high doses of corticosteroids, plasmapheresis, immunoglobulins, propofol, lidocaine, ketamine, inhaled desflurane, ketogenic diet, lacosamide, and therapeutic hypothermia were tried at different times in a period of 8 weeks, but all of them were ineffective. Electroconvulsive therapy (ECT) has been used in refractory SE in children. We report a case in which ECT was successfully used for treatment of refractory SE in a pediatric patient with FIRES syndrome.
Febrile infection–related epilepsy syndrome (FIRES) is a rare condition which evolves into refractory status epilepticus (SE), with poor outcome in most cases. Conventional antiepileptic drugs fail to control SE in FIRES patients. We report the case of a previously healthy 4-year-old boy who was diagnosed with FIRES. One week after pharyngitis and high fever he started seizures, followed by refractory SE. Benzodiazepines, phenytoin, high-dose barbiturates that induce burst suppression, high doses of corticosteroids, plasmapheresis, immunoglobulins, propofol, lidocaine, ketamine, inhaled desflurane, ketogenic diet, lacosamide, and therapeutic hypothermia were tried at different times in a period of 8 weeks, but all of them were ineffective. Electroconvulsive therapy (ECT) has been used in refractory SE in children. We report a case in which ECT was successfully used for treatment of refractory SE in a pediatric patient with FIRES syndrome.
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