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NTIS 바로가기생명과학회지 = Journal of life science, v.19 no.9 = no.113, 2009년, pp.1226 - 1231
Enzyme substitution with recombinant phenylalanine ammonia-lyase (PAL, EC 4.3.1.5) is currently being explored for treatment of phenylketonuria (PKU), an autosomal recessive genetic disorder with mutations of the gene encoding phenylalanine-4-hydroxylase (EC 1.14.16.1). However, oral administration ...
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